Abstract:Cerebral vascular malformations (CVM) are non-neoplastic lesions caused by abnormalities in the number and structure of brain vessels. Epileptic seizure is a frequent presenting symptom in patients with CVM, particularly in patients with brain arteriovenous malformations and cavernous malformations. CVMrelated epilepsy brings a series of burdens to patients, which is an essential factor to be considered in achieving a favorable prognosis for CVM. In this paper, we review the research advances in CVM-related epilepsy, including its incidence, pathogenesis, altered brain functional connectivity, risk factors, individualized evaluation, treatment, and prognosis, with the goal of assisting the diagnosis and treatment of CVM.